Tuesday, 2 February 2016

Alzheimers, Huntington's, ALS and Parkinson's Neurodegenerative Diseases


Can brain degeneration be combatted?


Neurodegenerative Diseases


Brain Degenerative Diseases such as Huntington’s, Parkinson’s, Amyotrophic Lateral Sclerosis (ALS) and all forms of dementia including Alzheimer’s are all classified as diseases affected by brain. Degenerative brain diseases have an enormous impact on our aging society. Alzheimer's disease progressively robs its victims of their memory. Parkinson's disease leads to impairments in movement. Frontotemporal (occurring the front area of the brain) dementia causes bewildering changes in a person's thoughts and behaviour. Huntington's disease painstakingly deprives a person of their ability to walk, talk, think and reason, often as early as in their mid-30s and 40s. In all of these degenerative brain diseases, the time from the onset of symptoms until death can be as many as ten or twenty years, with many sufferers' lives characterised by a total loss of independence in their final years.[i]




Over production of ROS (oxidative stress) is a central feature of all neurodegenerative disorders.[ii] There is strong evidence that mitochondrial dysfunction and oxidative stress plays a  role in neurodegenerative disease pathogenesis, including  four of the more well-known diseases Alzheimer's, Parkinson's, Huntington's, and Amyotrophic lateral sclerosis (ALS).[iii]

Alzheimer's Disease

Alzheimer's disease is characterised by loss of neurons (specialized nerve cells) and synapses (nerve cell signaling) in the cerebral cortex (outer layer of frontal part of the brain playing a role in consciousness) and certain subcortical regions (functional, connective and developmental areas of the brain). This loss results in gross atrophy (shrinkage) of affected areas of the brain.

Parkinson's Disease

Parkinson's disease is the second most common neurodegenerative disorder. Parkinson's disease is a degenerative disorder of the central nervous system. It results from the death of dopamine-generating (neuro-transmitter that send signals to other nerve cells).


Huntington's Disease


Huntington’s Disease causes astrogliosis (decrease of brain and spinal cord cells) and loss of neurons (specialized nerve cells).  Areas of the brain are affected according to their structure and the types of neurons they contain, reducing in size as they cumulatively  lose cells.


Amyotrophic Lateral Sclerosis (ALS) also commonly known as Lou Gehrig’s Disease


Amyotrophic lateral sclerosis (ALS or Lou Gehrig’s Disease) is a disease in which motor neurons are selectively targeted for degeneration affecting movement and speech.


Aging and Neurodegeneration


The greatest risk factor for neurodegenerative diseases is aging. Mitochondrial DNA mutations as well as oxidative stress both contribute to aging.  Many of these diseases are late-onset, meaning there is some factors that change as a person ages for each disease. One constant factor is that in each disease, neurons (specialized nerve cells) gradually lose function as the disease progresses with age.[iv]  Cell health is imperative to mitigate the damaging effects associated with degenerative disease.







[i] http://www.neuroscience.cam.ac.uk/research/cameos/DegeneratingBrain.php
[ii] https://en.wikipedia.org/wiki/Neurodegeneration
[iii] https://www.ncbi.nlm.nih.gov/pubmed/17051205
[iv] https://www.ncbi.nlm.nih.gov/pubmed/17051205

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